CASE REPORT
Laparoscopy in inguinal hernia and complete androgen insensitivity syndrome in children.
Whether and when to remove the gonads because of cancer?
Submission date: 2015-09-19
Final revision date: 2015-12-07
Acceptance date: 2015-12-11
Publication date: 2016-01-11
Medical Studies 2015;31(4):277-280
KEYWORDS
TOPICS
ABSTRACT
Androgen insensitivity syndrome (CAIS) – also called Morris syndrome, formerly known as testicular feminisation syndrome – is a congenital disorder of sex development caused by various mutations in the gene encoding the androgen receptor. Androgen insensitivity syndrome occurs in a complete form (complete androgen insensitivity syndrome – CAIS) or a partial form (partial androgen insensitivity syndrome – PAIS). In approximately 1% (according to various researchers, 0.8–2.4%) of cases of inguinal hernia in girls during the time before menarche, CAIS is seen. The laparoscopic procedure for inguinal hernia repair allows a visual assessment of the gonads, and possibly the collection of specimens from the gonads. This is much simpler, compared to the conventional procedure.
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| eISSN: | 2300-6722 |
| ISSN: | 1899-1874 |
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